Türk Nöroşirürji Dergisi
2010 , Vol 20 , Num 3
Fahr Diseases: Case Report
S.B. Dışkapı Yıldırım Beyazıt Eğitim ve Araştırma Hastanesi, 1. Beyin Cerrahisi Kliniği, Ankara, Türkiye
Fahr's is a familial disease which chracterized with presence of wide and
progressive calsifications in basal ganglions,cerebellar nucleus and deep cortical
anatomical structures.Metabolic disorders especially parathyroid disorders are
associated with Fahr disease.The clinical characteristics are very various and
usually appear such as disfunction of the affected areas.Common clinical findings
of the disease are progressive mental dysfunction, seizures, parkinson disease,
mood disorders and also may present without neurological abnormalities.This
kind of cases could be mimicking subarachnoid hemorrhage on admisson to
emergency clinic.The Brain Computed Tomography is the best useful diagnosis
method.In this report we assess Fahr disease which is a rare cause of intracranial
calsifications and could present with lots of neurological symptoms.
Anahtar Kelimeler :
Fahr disease, Intracerebral calcification, Radiological view