Türk Nöroşirürji Dergisi 2017 , Vol 27 , Num 3
Bilateral Coronal Synostosis: Brachycephaly
Ahmet KÜÇÜK1,Alper DURMUŞ1,Suat ÖKTEM1
1Erciyes Üniversitesi, Tıp Fakültesi, Beyin ve Sinir Cerrahisi Anabilim Dalı, Kayseri, Türkiye The premature fusion of both coronal sutures leads to a head shape called "brachycephaly." This causes restriction of growth of the anterior fossa resulting in a skull shape that is shorter and wider than normal. Enlarged supraorbital rim, flat and elongated frontal bone, occipital flattening, bitemporal protrusion, anteriorly shifted vertex, elongated skull and harlequin deformities can be present. This is followed by compensatory vertical growth called turricephaly. Bilateral coronal synostosis is often seen in patients with associated syndromes such as the Crouzon, Apert, Saethre-Chotzen, Muenke and Pfeiffer syndromes. These patients can also have additional sutures that are prematurely closed. Surgical treatment consists of fronto-orbital advancement and cranial vault reconstruction aimed at enlarging the anterior portion of the skull. Anahtar Kelimeler : Bicoronal, Brachycephaly, Synostosis