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¹Selçuk Üniversitesi, Tıp Fakültesi, Göz Hastalıkları Anabilim Dalı, Konya, Türkiye Craniosynostosis is characterized by premature closure of one or more cranial sutures. This developmental abnormality affects one child in every 2000 births. Premature closure of sutures may be seen as an isolated sporadic abnormality or may accompany syndromes, most of which are autosomal dominant. Non-syndromic cases are more frequently observed than syndromic cases. The most frequent syndromes have been reported as Apert, Crouzon, Pfeiffer and Saethre-Chotzen. Ophthalmic features may vary from mild hypertelorism to severe vision-threating strabismus, variable proptosis, optic atrophy and keratitis. The ophthalmologist should be part of the craniofacial surgical team in order to recognize the possible preventable causes of visual loss and determine the timing and extent of reconstructive surgery in those cases that are non-responsive to medical treatment. Anahtar Kelimeler : Hypertelorism, Craniosynostosis, Proptosis, Telecanthus