Türk Nöroşirürji Dergisi 2009 , Vol 19 , Num 2
Tethered Cord Syndrome Due to Sacral Agenesis Associated with Dextrocardia: Case Report
Özgür ÖZDEMİR1, Tarkan ÇALIŞANELLER2, Salih GÜLŞEN3, Aydın GERİLMEZ4, Elif KARADELİ5, Hakan CANER6
1,2,3,4,6Başkent Üniversitesi Nöroşirürji Anabilim Dalı Konya, Türkiye
5Başkent Üniversitesi Radyoloji Anabilim Dalı Ankara, Türkiye
Sacral agenesis is an aplastic vertebrae anomaly which is grouped under the family of caudal regression syndrome affecting lumbar and occasionally lower thoracal spinal segments. It is a very rare congenital anomaly in which gastrointesinal and genitourinary system malformations accompany the sacral or lumbosacral agenesis. Although, various congenital heart diseases could be observed in this disease, dextrocardia rarely develops. Early treatment of this patients is very important and recovery of the neurological symptoms related to the urgent interventions. In this report, we described a patient followed up for hydronephrosis with an unknown etiology and later diagnosed as tethered cord syndrome due to sacral agenesis associated with dextrocardia. Anahtar Kelimeler : Dextrocardia, Tethered cord, Caudal regression syndrome, Sacral agenesis