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¹Dicle Üniversitesi, Tıp Fakültesi, Endokrinoloji Bilim Dalı, Diyarbakır, Türkiye
²Dicle Üniversitesi, Tıp Fakültesi, Beyin ve Sinir Cerrahisi Anabilim Dalı, Diyarbakır, Türkiye
³Elazığ Özel Çağrı Tıp Merkezi, İç Hastalıkları Kliniği, Elazığ, Türkiye
⁴Dicle Üniversitesi, Tıp Fakültesi, Onkoloji Bilim Dalı, Diyarbakır, Türkiye
⁵Dicle Üniversitesi, Tıp Fakültesi, İç Hastalıkları Anabilim Dalı, Diyarbakır, Türkiye Pendred’s syndrome is characterized by congenital deafness and goiter and transmitted as an autosomal recessive disease. Thyroid dysfunction is related to an enzymatic defect in the organification of iodine. This defect can be detected by the perchlorate discharge test, which is diagnostic. The deafness is due to a congenital Mondini-type malformation of the cochlea. Pendred’s syndrome was diagnosed in our clinic together with acromegaly, a rare coincidence, and follow-up results are presented in light of the current literature. Anahtar Kelimeler : Pendred’s syndrome, Goiter, Acromegaly, Endoscopic surgery